Supporting Deaf Pupils with Additional Learning Needs
Presented on Tuesday, 18 January 2011
CHARGE syndrome
Wendy McCracken
C H A R G E
Multiple physical, sensory and behavioural anomalies
Every part of the auditory system may be affected
- External ear anomalies
- Middle ear anomalies, ossicular, chronic otitis media and chronic Eustachian tube dysfunction
- Under-development of the cochlea, and vestibular structures (Mondini's dysplasia)
- Reduced auditory nerve diameter
- Prolonged latencies
- Losses typically mixed with a very considerable conductive element
- Prevalence of severe-profound is approximately 50%
CHARGE syndrome
60% of children will acquire symbolic language
Mechanics of speech may be affected by cranio-facial abnormalities, breathing problems, and clefts
Success in acquiring symbolic communication has been found to be relate to the ability to walk independently by the age of 3 years
Behavioural issues are common and may be linked to:
- Multi-sensory impairments
- Communication frustrations
- Physical pain or discomfort
May be linked to cognitive impairment
Regulatory disorder, leading to problems with:
- Sleep-wake cycle [respite care]
- Hunger-satiety cycle
- Ability to console themselves
- Ability to plan their motor activity
Recent research suggests the presence of executive dysfunction, problems with:
- Shifting attention
- Initiating activity
- Inhibiting activity
- Sustaining activity
Functional communication is of central importance. Whatever system is put in place must be used at home as well as school.
Choosing a communication system
- Must include family
- Look at motor control-oro-motor and extremity
- User preferences
- Previous exposure
- CONSIDER a communication passport
- Practically usable
- Ergonomically acceptable
- Transportable
- Flexible
- Rate of use
- Possibility of extending
- User community
- Socially acceptable